Sleep-disordered Breathing in Neuromuscular Disease.

Daytime predictors of sleep disordered breathing in children and adolescents with neuromuscular disorders.

Sleep disordered breathing with or without nocturnal hypercapnic hypoventilation is a common complication of respiratory muscle weakness in childhood neuromuscular disorders. Nocturnal hypercapnic hypoventilation as a sign of respiratory muscle fatigue, portends a particularly poor prognosis. We aimed at identifying daytime predictors of sleep disordered breathing at its onset and sleep disorde...

Assessment of sleep-disordered breathing in pediatric neuromuscular diseases.

This is a summary of the presentation on the assessment of sleep-disordered breathing in pediatric neuromuscular diseases, presented as part of the program on pulmonary management of pediatric patients with neuromuscular disorders at the 30th annual Carrell-Krusen Neuromuscular Symposium on February 20, 2008.

British Thoracic Society guideline for respiratory management of children with neuromuscular weakness.

OF RECOMMENDATIONS Identifying children at risk of respiratory complications <Clinical assessment of respiratory health should be part of every medical consultation for children with neuromuscular weakness (NMW) and should be directed towards identifying progressive muscle weakness, ability to cope with respiratory infection, aspiration, progression of scoliosis and sleep-disordered breathing. ...

Screening for Pompe Disease in Specific At-Risk Populations with Sleep-Disordered Breathing.

Sleep and breathing in neuromuscular disease.

Respiratory muscle weakness in neuromuscular disease causes significant morbidity and mortality. The published data on respiratory muscle activity and breathing during sleep in normal subjects, the impact of respiratory muscle weakness on sleep and breathing and the relations to daytime respiratory function in neuromuscular disease are reviewed here. In normal subjects during sleep upper airway...